Comprehensive Surgical Management of Congenital Heart Disease

Highly Commended, BMA Medical Book Awards 2015 Since the first edition of this book was published in 2004, the management of congenital heart disease has continued to evolve at a rapid pace. Not only have new operations been developed and expanded, such as the intra/extracardiac conduit Fontan and the double root translocation for corrected transposition, but in addition, diagnostic methods—particularly cardiac CT and MRI—have been dramatically transformed. Understanding of the genetic basis of congenital heart disease and the embryology of cardiac development has progressed even more rapidly. What has not changed is that optimal outcomes for children and adults with congenital heart disease can only be achieved by a collaborative team effort. The team includes not only congenital cardiac surgeons but also pediatric cardiac nurses, pediatric cardiologists, perfusion and respiratory technicians, pediatric cardiac intensivists, pediatric cardiac anesthesiologists, ultrasonographers, and MRI and catheter laboratory technicians. This second edition of Comprehensive Surgical Management of Congenital Heart Disease describes in detail the contemporary practice of Richard A. Jonas and the cardiac team at Children’s National Medical Center in Washington, D.C. The book once again includes numerous beautiful illustrations providing comprehensive and detailed information about intra-operative management of the entire spectrum of congenital heart surgery. In addition, the companion VitalSource ebook contains more than 50 operative videos that have been edited and narrated to highlight the key steps in complex surgical procedures. The book incorporates an evidence-based approach, supported throughout by numerous scientific citations, to explain when and why an operation should be done as well as the risks, benefits, and potential complications.

Background Why early primary repair Surgical technique Biomaterials for congenital cardiac surgery Anesthesia for congenital heart surgeryPediatric cardiac intensive careCardiopulmonary Bypass The bypass circuit: hardware optionsPrime constituents and hemodilution Carbon dioxide, pH and oxygen management Hypothermia, reduced flow and circulatory arrest Myocardial protection Specific congenital cardiac anomalies Patent ductus arteriosus, aortopulmonary window, sinus of Valsalva fistula, aortoventricular tunnel Coarctation of the aorta Atrial septal defect Ventricular septal defect Transposition of the great arteries Tetralogy of Fallot with pulmonary stenosis Valve surgery for congenital heart disease Left ventricular outflow tract obstruction: aortic valve stenosis, subaortic stenosis, supravalvar aortic stenosis Hypoplastic left heart syndrome Single ventricle Complete atrioventricular canal Anomalies of the pulmonary veins Double outlet right ventricle Truncus arteriosus Tetralogy of Fallot with pulmonary atresia Pulmonary atresia with intact ventricular septum Interrupted aortic arch Congenitally corrected transposition of the great arteries Vascular rings, slings, and tracheal anomalies Anomalies of the coronary arteries

Richard A. Jonas MD is the Co-director of the Children’s National Heart Institute in Washington, D.C. He is the Cohen-Funger Professor of Surgery at Children’s National Medical Center and Professor of Surgery at George Washington University. He is also past president of the American Association for Thoracic Surgery and the Congenital Heart Surgeons’ Society.